• Tetralogy of Fallot with Absent Pulmonary Valve
    • Anterior deviation of the conal septum into the RVOT (starred structure)
    • Large conoventricular VSD
  • Tetralogy of Fallot with Absent Pulmonary Valve
    • Hypoplastic pulmonary valve oriface
    • Severely dilated branch pulmonary arteries
  • Tetralogy of Fallot with Absent Pulmonary Valve
    • Turbulent flow across hypoplastic pulmonary valve oriface 
    • Severe pulmonary regurgitation
    • Dilated branch pulmonary arteries
  • Tetralogy of Fallot with Absent Pulmonary Valve
    • Continuous wave Doppler across the pulmonary valve
    • Moderate pulmonary stenosis (below baseline) with a peak velocity of ~3.7 meters/sec with a peak gradient of ~56 mmHg.
    • Free pulmonary regurgtiation (flow above baseline)
  • Tetralogy of Fallot with Absent Pulmonary Valve 
    • Turbulent flow across the pulmonary valve oriface
    • Severely dilated main and branch pulmonary arteries