• Tetralogy of Fallot with Absent Pulmonary Valve
    • Mild right ventricular hypertrophy 
  • Tetralogy of Fallot with Absent Pulmonary Valve
    • Large conoventricular VSD
    • Overriding aorta
  • Tetralogy of Fallot with Absent Pulmonary Valve
    • Anterior deviation of infundibular septum into the RVOT (denoted by star)
    • Large VSD
  • Tetralogy of Fallot with Absent Pulmonary Valve
    • Pulmonary stenosis
    • Severe pulmonary regurgitation
    • Infundibular septum deviated into the RVOT (denoted by the star)
    • Large conoventricular VSD
    • Severely dilated right pulmonary artery
  • Tetralogy of Fallot with Absent Pulmonary Valve
    • Hypoplastic pulmonary valve annlus 
    • Severely dilated branch pulmonary arteries
  • Tetralogy of Fallot with Absent Pulmonary Valve
    • Hypoplastic pulmonary valve annlus 
    • Severely dilated branch pulmonary arteries
    • Severe pulmonary regurgitation (red color Dopplet jet)
    • Pulmonary stenosis (turbulent flow noted at site of pulmonary annulus)
  • Tetralogy of Fallot with Absent Pulmonary Valve
    • Hypoplastic pulmonary valve annlus 
    • Severely dilated branch pulmonary arteries
  • Tetralogy of Fallot with Absent Pulmonary Valve
    • Hypoplastic pulmonary valve annlus 
    • Severely dilated branch pulmonary arteries
    • Pulmonary stenosis (turbulent red color Doppler flow noted at site of pulmonary annulus)
    • Pulmonary regurgitation (blue color Doppler jet at site of valve annulus)
  • Tetralogy of Fallot with Absent Pulmonary Valve
    • Spectral Doppler across the pulmonary valve revealing pulmonary stenosis (below baseline) and severe pulmonary regurgitation (above baseline)

This is Tetralogy of Fallot with Absent Pulmonary Valve