• Double Inlet Left Ventricle (left-handed ventricular topology, L-TGA)
    • Apical view demonstrating left AV valve chordae seen beneath the pulmonary valve and crossing the VSD into hypoplastic subaortic outlet chamber
    • The pulmonary valve appears thickened with tethered leaflets
  • Double Inlet Left Ventricle
    • Apical view demonstrating two AV valves aligned and connected to a single morphologic left ventricle with fine apical trabeculations
  • Double Inlet Left Ventricle (right-handed ventricular topology, D-TGA)
    • Apical view demonstrating parallel great arteries
    • The aorta appears rightward and arises from the small outlet chamber
  • Double Inlet Left Ventricle (right-handed ventricular topology, D-TGA)
    • Apical color Doppler demonstrating parallel great arteries
    • The aorta appears rightward and arises from the small outlet chamber
    • Trivial aortic regurgitation
  • Double Inlet Left Ventricle (right-handed ventricular topology, D-TGA)
    • Apical sweep demonstrating two AV valves connected to the single left ventricle
    • The pulmonary artery arises from the left ventricle (is seen as the bifurcating vessel)
    • The aorta appears rightward and arises from the small outlet chamber (seen briefly at end of sweep)
  • Double Inlet Left Ventricle (right-handed ventricular topology, D-TGA)
    • Color compare view
    • Left atrial enlargement
    • Flow turbulence across left AV valve
    • Small restrictive atrial communication with small amount of left to right shunting
    • Findings overall suggestive of left atrial hypertension and a restrictive ASD
  • Double Inlet Left Ventricle 
    • Continuous wave Doppler across the left AV valve with left AV valve stenosis with a mean gradient of 10 mmHg
    • Patient with left atrial hypertension with left AV valve stenosis and a restrictive ASD
  • Double Inlet Left Ventricle (right-handed ventricular topology, normally related great arteries, aka Holmes heart)
    • Apical sweep demonstrating two AV valves aligned and connected to the single left ventricle
    • Sweeping anteriorly demonstrates normally related great arteries
    • The aorta arises posteriorly from the single left ventricle
    • The pulmonary artery arises anteriorly (at end of sweep) from small right sided anterior outlet chamber
  • Double Inlet Left Ventricle (right-handed ventricular topology, normally related great arteries, aka Holmes heart)
    • Apical color Doppler sweep demonstrating two AV valves aligned and connected to the single left ventricle
    • Sweeping anteriorly demonstrates normally related great arteries
    • The aorta arises posteriorly from the single left ventricle
    • The pulmonary artery arises anteriorly (at end of sweep) from small right sided anterior outlet chamber
  • Double Inlet Left Ventricle
    • Right and left AV valves both empty into a dilated left ventricle
  • Double Inlet Left Ventricle
    • Right and left AV valves both empty into a dilated and trabeculated left ventricle

Apical 4 chamber view.