• Scimitar Syndrome
    • Anomalous right pulmonary vein seen entering near IVC-RA junction
  • Scimitar Syndrome
    • Anomalous right pulmonary vein (red flow) seen entering near IVC-RA junction
  • Scimitar Syndrome
    • Anomalous right pulmonary vein (red flow) seen entering near IVC-RA junction
  • Scimitar Syndrome
    • Two anomalous right sided pulmonary veins draining near IVC-RA junction
  • Scimitar Syndrome
    • Anomalous right pulmonary vein (red flow) seen entering near IVC-RA junction
  • Scimitar Syndrome
    • Spectral Doppler in the anomalous right pulmonary vein revealing an unobstructed venous Doppler pattern with a mean gradient ~1 mmHg.
  • Echocardiographic Assessment: Subcostal IVC
    • Assess for anomalous venous drainage near IVC-RA junction (2D +C)
    • Spectral Doppler of any abnormal structures entering IVC-RA to assess Doppler waveform (venous pattern) and for evidence of stenosis (assess mean gradient by spectral Doppler)