Primary cardiac tumors in infancy and childhood are uncommon, and approximately 70% of them are benign with morbidity rate of around 0.27% to 0.8%. Cardiac fibromas, which normally arise from heart fibroblasts or myofibroblast, accounts for around 2% to 5% of all benign tumors in the heart. They represent the second most common cardiac tumors in infancy but rank first in surgical series. Complications can include inflow and outflow tract obstruction, valvular dysfunction and ventricular arrhythmias. Fibromas are most commonly located in the ventricular septum, but they may occasionally be found in the ventricular free wall. Gadolinium enhanced MRA and first pass perfusion imaging demonstrate a hypoperfused tumour core that is readily distinguishable from the surrounding perfused myocardium.